Malignant neoplasms composed of MACROPHAGES or DENDRITIC CELLS. Most histiocytic sarcomas present as localized tumor masses without a leukemic phase. Though the biological behavior of these neoplasms resemble lymphomas, their cell lineage is histiocytic not lymphoid.

A rare, usually progressive disorder comprising an invasive proliferation of neoplastic HISTIOCYTES. Many previous cases are now thought to represent ANAPLASTIC LARGE-CELL LYMPHOMA.

Synonyms: Malignant Histiocytosis, Sarcoma, Histiocytic, True Histiocytic Lymphomas, Malignant Histiocytoses, Histiocytic Lymphoma, True, Histiocytic Sarcoma, Lymphoma, True Histiocytic, Histiocytosis, Malignant, True Malignant Histiocytoses, True Malignant Histiocytosis, Histiocytosis, True Malignant, Histiocytic Lymphomas, True, Sarcomas, Histiocytic, Malignant Histiocytoses, True, Lymphomas, True Histiocytic, True Histiocytic Lymphoma, Histiocytic Sarcomas, Histiocytoses, True Malignant, Malignant Histiocytosis, True, Histiocytoses, Malignant

Instance information

comment

2008; for HISTIOCYTOSIS, MALIGNANT see HISTIOCYTOSIS, MALIGNANT 1987-2007 ,2008

identifier

D054747

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