A syndrome characterized by lesions occurring on the face, scalp, or neck which consist of congenital hypoplastic malformations of cutaneous structures and which over time undergo verrucous hyperplasia. Additionally it is associated with neurological symptoms and skeletal, ophthalmological, urogenital, and cardiovascular abnormalities.
Synonyms: Feuerstein Mims Syndrome, Linear Verrucous Epidermal Nevus, Linear Sebaceous Nevus, Jadassohn Sebaceous Nevus, Nevus, Sebaceous of Jadassohn, Jadassohn Nevus Sebaceus, Inflammatory Linear Verrucose Epidermal Nevus, Syndrome, Schimmelpenning, Nevus, Verrucous Epidermal, Syndrome, Feuerstein-Mims, Nevus Phakomatoses, Organoid, Sebaceous Nevus Syndrome, Linear, Schimmelpenning Feuerstein Mims Syndrome, Nevus Sebaceus of Jadassohn, Syndrome, Schimmelpenning-Feuerstein-Mims, Sebaceous Nevus of Jadassohn, Nevus Phakomatosis, Organoid, Schimmelpenning Syndrome, Verrucous Nevus, Nevus Phakomatosis, Jadassohn, Jadassohn Nevus Phakomatosis, Phakomatoses, Organoid Nevus, Verrucous Epidermal Nevus, Schimmelpenning-Feuerstein-Mims Syndrome, Linear Sebaceous Nevus Syndrome, Phakomatosis, Jadassohn Nevus, Feuerstein-Mims Syndrome, Nevus, Linear Sebaceous, Organoid Nevus Phakomatoses, Nevus, Verrucous, Sebaceous Nevus, Linear, Organoid Nevus Phakomatosis, Epidermal Nevus, Verrucous, Phakomatosis, Organoid Nevus, Inflammatory Linear Verrucous Epidermal Naevus
Instance information
2010 (2008) ,2010; see NEVUS SEBACEOUS OF JADASSOHN 2008-2009
D054000